Sieiro Santos
Sjögren’s syndrome is a systemic autoimmune disease caused by lymphocytic infiltration of exocrine glands causing sicca syndrome. It can affect extra-glandular organs such as the lungs which can result in diffuse interstitial lung disease, a well-known form of lung involvement.
In pediatric patients, Sjögren’s syndrome is less common that in adult patients and often associates more heterogeneous presentations.